Autopsy and Case Reports
Autopsy and Case Reports
Clinical Case Report and Review

Renal angiomyolipoma with epithelial cyst

Bharti Varshney; Vikarn Vishwajeet; Vijay Madduri; Gautam Ram Chaudhary; Poonam Abhay Elhence

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Angiomyolipoma with epithelial cysts (AMLEC) is a recently described entity and is an uncommon subtype of kidney angiomyolipomas. AMLEC is a benign entity but usually masquerades a renal cell carcinoma on imaging examination. AMLEC has a distinct histological and immunohistochemical staining pattern, which helps in the pathological diagnosis. We present a rare case of AMLEC in a 26-year-old female, which was provisionally diagnosed as renal cell carcinoma on radiology. We also summarize the differential diagnosis of this rare variant, its characteristic features, and a review of the literature.


Angiomyolipoma, Neoplasms, Kidney, Nephrectomy, Diagnosis, Differential


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